Artikel
Neurophysiologic results in infants with auditory neuropathy/dys-synchrony related to cochlear implant candidacy
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Veröffentlicht: | 31. Mai 2005 |
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Gliederung
Text
Patients with auditory neuropathy (AN) present with significant sensorineural hearing loss, poor speech perception and impaired temporal processing. The diagnosis is based on discrepancies between different objective measures: cochlear microphonics and otoacoustic emissions are present indicating unimpaired outer hair cell function, the auditory brainstem response and the cochlear nerve action potential are absent. There have been reports on children with a diagnosis of AN who have benefited from cochlear implantation, as well as reports of hearing recovery in patients with a diagnosis of AN. This presentation demonstrates that similar initial clinical result patterns may have different final outcomes: in particular, when associated with hyperbilirubinemia, the "typical" AN test results may be reversible. In other cases, they persist and the patient is a cochlear implant candidate. We will also demonstrate the value of the perioperative, transtympanic, electrically-evoked ABR in AN patients.